Ukubaluleka kwezifo zesifo se-cystic kugqitywe yizinto ezilandelayo:
• Ii-cysts zivame kakhulu kwaye ngamanye amaxesha zimelela umsebenzi wokuxilonga obunzima kumayeza-abagqirha, oogqirha, abadumi be-radiologists kunye ne-pathologists.
• Ezinye iifom, ezifana nesifo sezintso ze-polycystic kubantu abadala, sisona sizathu esibalulekileyo sokubandakanya isigulane kwiprogram ye-hemodialysis.
• Ama-cyst angagcina aphendule ngamathumba ezibi anzima ukuzibona.
I-cysts elula
I-cysts elula yenziwe ngama-cystic formations of different size, ukusuka kwi-1 ukuya kwi-10 cm ububanzi. Iingqumbo zivame ukujikelezwa ngegobolondo ephosa imbala kwaye izaliswe ngokucacileyo. Kwizintso, ii-cysts zihlala zihlala kwindawo ye-peripheral (kwindawo ye-cortex), nangona ngamanye amaxesha zingabakho kwindawo ephakathi (kwi-medulla). Amagqabha ezintsheni, njengomthetho, angabangeli naziphi na iimpawu kwaye eziqhelekileyo kubantu abadala kuneminyaka engama-50. Ngobuninzi bee-cyst, intlungu kwi-lumbar esifundeni iyakwenzeka, kodwa i-cysts idla ngokubonakala ngengozi xa ihlola izintso zenye i-pathology. Iziganeko zokuqhwala kwii-cysts zichazwe, esi sigulane siziva ngathi ubuhlungu obukhawuleza kwiindawo ezisecaleni kunye nendawo. Ukuhlambalaza kunokuba ngummemezeli wesifo esibi kakhulu segolide ye-cyst. Ngomntwana ozalwe ngumntwana we-kidticystosis yeentso, umntwana uzalwe ngeentso eziphuculweyo ezingekho zokusebenza, into leyo eguqulelwe ibe yinkitha yama-cyst. Ngomonakalo wentshonalanga, i-fetus i-utero ayikwazi ukuvelisa umchamo, okubangele ukuba i-amniotic encinci. Oku kukukhokelela ekutshatyalaliswa komntwana ngenxa yokunyuka kwengcinezelo yesisu. Ubuso besiqhamo esinjalo sihlambulukile, impumlo iphotshiwe, iindlebe ziphantsi, kunye neentloko eziphantsi phantsi kwamehlo.
Ukususwa Kwezintso
Izigulane ezinengqondo ze-multicystic zicetyiswa nge-nephrectomy - ukususwa kweentso. Umsebenzi uyenzeka xa ukwanda okanye usulelo lwe-cysts, kunye nokuxinzelelo lwegazi kwi-patient.
I-Polycystic yimeko yesimo somzimba. Kukho iintlobo ezininzi zesifo:
• Ukubeleka komntwana - umntwana uzalelwa ezintso ezinkulu aze afe emva nje kokuzalwa;
• abangabantwana abathatywayo-bafumaneka kwinyanga yokuqala yokuphila;
• Abantwana-kubantwana abaneminyaka engama-3 ukuya kwe-12 ubudala, kukho i-gap yophuhliso kunye nokungaphumeleli kwezintso. Ezinye iimpawu zibandakanya uxinzelelo lwegazi oluphezulu, ukwandiswa kwesibindi kunye nepeni;
• abantwana - isifo sifumaneka ngexesha leminyaka yokuqala yobomi;
• Abadala - le meko ikhula kubantu abathwala abantu abadala be-autosomal gene gene. Oku kuthetha ukuba umntu ogulayo uyayifumana ilifa lomzimba wesifo kumnye wabazali.
Isifo esiphezulu se-genetic kwi-polycystic isifo sesifo kubantu abadala kuguquka kwi-chromosome yesi-16, ejongene nokuveliswa kweprotheni ye-polycystin. Le nxalenye yokugqibela ibambe iqhaza elibalulekileyo ekusebenzisaneni kwe-intercellular. Iimpawu zezintso ze-polycystic ziquka ukuqhaqhaqhaqha, intlungu kwi-lumbar esifundeni, i-hematuria (igazi kumchamo) kunye negazi eliphezulu. Umonakalo wezintso ungabonwa ngengozi okanye ngenxa yeziphumo zezilwanyana zesigulane.
Diagnostics
Kwizigulane ezininzi, isifo sifumaneka kwiminyaka engama-30 ukuya kuma-50. Ukunciphisa ngokukhawuleza kwento yokuguqulwa kwengqondo kubonwa malunga nesithathu kwezigulane kwaye kukhokelela kwisidingo sokudwelisa i-dialysis, kwaye emva koko ukuguqulwa kwezintso.
Izimpawu ezihambelanayo
I-Polycystic inokuhamba kunye neminye impawu ezinokugula, ezibandakanya, ngokukodwa:
• uxinzelelo oluphezulu (uxinzelelo lwegazi oluphezulu);
• Ukunyanga kwama-cysts;
• ii-aneurysms (inqwaba eludongeni) yengqondo kunye nezinye iirriyiti;
• I-Hernias kunye ne-diverticula yamathumbu.
Unyango
Izigulane kwi-dialysis okanye emva kokufakelwa kwintsholongwane zingadinga ukususa iinyoko ezikhulayo ukwenzela ukukhusela ukuphuma kwegazi, usulelo kunye nentlungu.
Ezinye izifo zesifo seengqondo ziquka:
• I-Fanconi syndrome yimeko engavumelekanga, izuzwe njenge-X ehlanganisiweyo. Ifana ne-anemia, ukuhluleka kwezintso kunye ne-sodium ephantsi egazini.
• Intso yesipongy - ukwandiswa okubukhali kokuqokelela iibhubhu. Inxalenye encinci, iinjongo okanye zonke iinjongo zombini zinokuchaphazeleka. Le meko yokuzalwa okanye efunyenwe ngokuqhelekileyo idibaniswa kunye ne-tumor yeWilms (isifo sezintso ezinobungozi kubantwana), i-aniridia (ukungabikho kwe-iris kweso) kunye ne-hemyhypertrophy (hypertrophy yezihlunu zesigamu somzimba). Esi sifo sihlala sihamba kunye nezifo ezithintekayo zokungena kumanzi, ukubunjwa kwamatye kunye nokuhluleka kwezintso.
Isifo se-Hippel-Lindau sisifo esibalulekileyo sentsapho ekuphuhliseni izicubu ezinobungozi ze-cerebellum, i-retina, umgudu, ngamanye amaxesha i-pancreas kunye ne-adrenal gland kwimeko yomonakalo we-cystic ye-kidney, ekhokelela ekungcoleni.
• Ama-cyst of malin of the kid is the result of the destruction of the part of the tumor's cancer and the formation of cyst or, in contrast, the malignancy of a bladder cyst.