Indlela yokuphatha isifo sezintso ze-polycystic?

Leyo binzana i-polycystic kidso ibhekisela kubukho bama-cysts amakhulu ezintso. Ukuba udibanisa ngqo nesigama, isifo sesifo se-polycystic isifo esisasazekayo ekuzalweni, oko kukuthi, ukuzalwa komntwana kunye nokubonakalisa ubukho bama-cysts kwiintlobo zombini. Esi sisona siphene esibonakaliswe ngokugqithiseleyo solu hlobo kwaye asihlanganiswanga rhoqo kunye neziphoso ezifanayo, isibindi se-polycystic kunye nesifo seplatocystic pulmonary. Isifo sisimo semvelo, oko kukuthi, yonke intsapho iyagula, njengomthetho. Ngokuqhelekileyo kwi-polycystosis zintlungu zombini. Kule meko, ukubunjwa kwee-cyst kwenzeka kwiqonga lezintso zesibini, okubangelwa ukungasebenzi kwemisebenzi ye-secretary encinci ye-nephron. Okokuthi, iimeko ezinjengeentliziyo ze-polycystic zikhokelela kwisifo se-stalosis ye-renal tubules kunye nokwanda kwengcinezelo kubo. Ama-cyst azinziwe aqukethe urea, i-uric acid, i-salts kunye nezinye iimveliso zegazi. Ukunyanzeliswa kwezicubu zeengso kunye ne-cysts kubangela ukuba i-oxygen yalala yindlala kunye nobomi bexesha lonke. Kwaye ke, emva kweenkcukacha ze-anatomical, sinokuqwalasela indlela yokuphatha i-polycystosis yeentso, kunye ne-etiology yesifo, iklinikhi kunye ne-symptomatology yesifo kwaye, ngokuqinisekileyo, unyango lwezintso ze-polycystic.

I-pathologically, kukho iintlobo ezimbini zezi zifo: abadala kunye nabantwana. Intso yePolycystic inokwenzeka nge-autosomal gene gene, oko kukuthi, idlulelwe kumzali ukuya kumntwana, kakuhle, okanye ilifa ngohlobo lwe-autosomal-resistive genes, oko kukuthi, xa abazali bobabini bezothatha isifo. Isifo sezintso zePolycystic senziwa ngenxa yokuphulwa kwesakhiwo sezintso okanye ukubunjwa kwayo kunye ne-bookmarking ngexesha lokubeleka, kwaye ngamanye amaxesha livelisa inani elincinci leeseli ezifunekayo kwintsebenzo yesifo. Ama-Cysts akhiwa xa kukho ukungabikho kokungaqhelekanga koxhumo phakathi kweethubhu ze-renal ngqo kunye ne-glomeruli okanye xa zikhubazekile.

Yiyiphi impawu ekwazi ukukholisa phambi kwesi sifo kwaye uncede ukuqonda: indlela yokuphilisa i-polycystosis yeentso zale okanye ukuba isantya sokungahoywa? Ezi ziimpawu ezinjengeentlungu ezinzima kunye neentlungu ezihlala kwingingqi ye-lumbar, uxinzelelo lwegazi oluphezulu, isicaphulelo kunye nokuhlanza. Olu luhlu lweempawu ezibonisa ukuba isigulane ngokwakhe, kwaye iimpawu ezichazwe kwiibhoratri ziquka ukubonakaliswa kweempawu zentsholongwane egazini (i-leukocytosis, i-lymphocytosis, i-ESR iyakwanda kancane) kunye ne-hematuria (igazi emcinini) kunye ne-pyuria (i-pus in the urine). Kwiklinikhi, ngokufutshane, unokuthetha amagama ambalwa. Inkcazo yeembonakaliso zeklinikhi kule meko kubaluleke kakhulu, njengoko, njengoko kuya kubhalwa ngezantsi, unyango lweentso ze-polycystic luphawu, oku kuthetha ukuba iziyobisi zikhethwe ukuba zisuse iimpawu zesifo. Kwaye ke, intso ye-polycystic kubantwana abancinci imbi kakhulu, ngokuqhelekileyo i-forecast isingathandekiyo, isiphumo sesi sifo kukufa komntwana kwi-uremia (ubuthi-bungozi bomzimba ngenxa yobunzima bomzimba). Kubantu abadala, isifo sezintso ze-polycystic sidlulayo ngokuthe ngcembe kwaye senziwe ngokwahlukileyo sibe ngamanyathelo amathathu: umvuzo, ukuxhaswa kwemali, ukuhlawulwa kwemali. Icandelo ngalinye linempawu zalo. Kwisigaba sokuqala se-polycystic isifo sesifo, oko kukuthi, kwinqanaba lembuyekezo, izibonakaliso azibonakalwanga kwaye, ngokufanelekileyo, akukho zikhalazo ezivela kwisigulane kuza. Kwinqanaba lesibini, ukuxhaswa kwemali, kukho imbonakalo yokungaphumeleli kwindlala. Kukho unxano olubuhlungu, umlomo owomileyo, ukunyuka kwengqondo kunamandla, ukwanda kwengcinezelo yegazi kuya kuba nzima. Kukho i-pyesis yama-cyst, ehamba kunye ne-chills, i-fever, ekuhlalutheni kwe-leukocytosis yegazi kunye ne-ESR eyandisiweyo. Amatye angabakho kwizintso angabangela ukuxhamla kwe-coal renal. Kwaye xa isifo sifika kwisigaba sesithathu, i-uraemia iyaqhubeka. Kule nqanaba, lesi sifo sinokuphucula kunezona zimbini zangaphambili. Le meko iphela iminyaka, ekhokelela ekuphuhlisweni kokungaphumeleli kwindlala. Ukungonakaliswa ngokukhawuleza kwimeko yesigulane kwenzeka ngokukhawuleza emva kokuqhotyosheliswa kosulelo lwesibini, umzekelo, i-SARS, i-influenza njalonjalo. Ngelishwa, emva kokuxilongwa kwe-polycystic isifo sesifo, ubomi bezigulane ngumlinganiselo ongaphantsi kweminyaka eyi-15.

Ngokuphathelele unyango lweentso ezichaphazelekayo yi-polycystosis, iphathwa ngokuphawulekayo, oko kukuthi, akukho nonyango olufanelekileyo olufanelekileyo kubo bonke. Ukuba isigulane asikuthi, kwaye kwakungenako ukuphelelwa yintsholongwane engapheliyo, ngoko ugqirha umisela ukutya okunotyebileyo. Ukuze uxinzelelo lwegazi lube nomyalelo wokunciphisa uxinzelelo lwegazi, ukuba isigulane i-pyelonephritis, iziyobisi kunye neziyobisi ze-uroseptic ziyachongwa. Ukuxhaswa kwama-cyst kunye nobukho bamatye kwiiblule zingadinga ukungenelela ngonyango. Ukuba kuphela i-cysts enye ifunyenwe, yikhuphe kuphela umbane ngokugqithisa. Le nkqubo yenziwa phantsi kwe-anesthesia. Emva kokulahlekelwa ngumzwelo, inaliti engagxinyiweyo, isalathisi iyahlanjululwa ngokubhoboza iinjongo, kwaye i-fluid iyasondliwa, inaliti efanayo iya kuthathwa uviwo. Akusoloko le ndlela yonyango isusa zonke iimpawu zesifo nokuphulukiswa kwesiqinisekiso, imeko yesigulane, iklinikhi yesi sifo ixhomekeke kwiikristi ngokwabo, ubungakanani babo, umonakalo. Eyona nto ibuhlungu kakhulu, ukuba iinjongo zilahlekelwa ukukwazi ukucoca umchamo, ngoko iimpiliso yokufakelwa kunye ne-hemodialysis iyadingeka, ezayo ekukhokelela ekunyusweni kwentliziyo. Ngelishwa, kwesi sifo, ukuzithemba kwodwa kunokukhathaza imeko yesigulane kunye nekhosi yokugula. Kukho naziphi na iimeko, ukuphulwa komsebenzi weentso kufuneka kuthethane nangoko ugqirha. Ngentlungu kwindawo ehlala kuyo, i-hematuria kunye nobukho be-urinary infection, akufanele uhambe ugqirha. Ewe, njengendlela yokukhusela, unokufumanisa ukuba unayo izalamane kwintsapho yakho eye yabhekana okanye isifo se-polycystic isifo. Ekubeni kweso sifo, kufuneka ufunde uroloki kwaye ungabhalisi ngokukhawuleza. Khumbula ukuba ngesimo sengqondo sokungahoywa okanye sokunyaniseka ngesigulo, isiguli sinethuba (25%) ukuhambisa lesi sifo kumntwana ozayo.